GEPATOSEREBRAL DEGENERTSIYA: KASALLIKNING AYRIM KLINIK HOLATI
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gepatoserebral degeneratsiya, jigar sirrozi, marganets toksikligi, bazal gangliyalar, kam uchraydigan nevrologik kasallik, Vilson-Konovalov kasalligi, genetika, klinik ko'rinish, diagnostika, davolashAbstrak
Olingan gepatoserebral degeneratsiya deb ham ataladigan gepatoserebral degeneratsiya surunkali jigar kasalligining kam uchraydigan nevrologik asoratidir. Bu markaziy asab tizimida marganets va ammiak kabi neyrotoksik moddalarning to'planishi natijasida yuzaga keladi, birinchi navbatda bazal ganglionlarga ta'sir qiladi. Kasallik ekstrapiramidal alomatlar, tremor, qattiqlik, kognitiv buzilish va ruhiy kasalliklar sifatida namoyon bo'ladi. Ushbu maqolada surunkali jigar sirrozi bilan og'rigan 52 yoshli erkakda gepatoserebral degeneratsiyaga mos keladigan progressiv nevrologik alomatlar paydo bo'lgan klinik holat keltirilgan. Diagnostik tasvirlar, laboratoriya natijalari va davolash strategiyasi tasvirlangan. Hisobotda miyaning qaytarilmas shikastlanishining oldini olish uchun erta aniqlash va multidisipliner davolash muhimligi ta'kidlangan.
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